PNET (Primitive Neuroectodermal Tumor)
The term primitive neuroectodermal tumor or PNET is
a relatively new term that is used to describe a group
of tumors. In these tumors, the type of cell seen is
very similar. Their locations are quite different. Tumors
that fall under the heading PNET include medulloblastoma
(the most common), pineoblastoma, ependymoblastoma,
retinoblastoma, neuroblastoma
and esthesioneuroblastoma. Other than the medulloblastoma,
these are all rare tumors. These tumors generally occur
in children.
PNET (Primitive Neuroectodermal Tumor) Symptoms
The symptoms of the PNET group of tumors are related
to their size and location. Commonly, they cause increased
pressure inside the head. This can result in headache,
nausea and vomiting. Other symptoms result from pressure
on the brain itself and can result in weakness, visual
problems and loss of balance. Seizures are common.
PNET (Primitive Neuroectodermal Tumor) Diagnosis
As always, the first steps in diagnosis are a careful
history and physical examination. CT
or MRI scanning performed
without and with intravenous contrast enhancement are
the next step. Because of the possibility of spread
through the spinal fluid, MRI of the entire spine is
frequently performed.
PNET (Primitive Neuroectodermal Tumor) Treatment
Surgery is the usual first treatment for these tumors.
They are generally unable to be cured by surgery. Further
treatment with radiation
therapy is the usual next step. For children under the
age of three years, chemotherapy may be given instead
of radiation therapy. Chemotherapy may also be used
as additional treatment in older patients.
Call 1-800-411-CINN or the location
nearest you between 8 AM and 5:30 PM Central
Time, Monday through Friday to schedule an initial consultation
with a CINN
physician.
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